CT
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Collagen






Alport

Collagen Synthesis




Scurvy


- propeptide added to fibrillar collagens




Pathology


Osteogenesis





Ehlers Danlos




Menke


Elastin




AAT

Williams

- elastin important component of aorta
Fibrillin

Marfan


- CT abnormal, allow pts to grow very tall with long arms





- weak aortas because weak elastin from fibrillin deficiency

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