CT
typora-copy-images-to: ./images
![](https://photos.thisispiggy.com/file/wikiFiles/6971B970-F59A-4E29-ABC1-FDD18C19A22A.jpg)
Collagen
![](https://photos.thisispiggy.com/file/wikiFiles/0DA54C0B-E8CE-47B8-ACD5-503E38999103.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/7AF93930-DC8B-4054-9F98-3344C2AFD8E4.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/B810DFC5-AD5A-49BD-A0CA-F4BB6C223477.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/4262B72F-A299-4AC6-A306-835F8D3B6077.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/6B804F30-E01B-4B67-9A2D-F26973FA86CA.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/01F39535-24BE-4DAA-9394-C01FEB49A81F.jpg)
Alport
![](https://photos.thisispiggy.com/file/wikiFiles/8C57E300-EB3B-4004-8E62-5F2FBDC5EC1E.jpg)
Collagen Synthesis
![](https://photos.thisispiggy.com/file/wikiFiles/7870BFA2-B00B-4B34-9784-612357C18311.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/D720916A-FE24-4196-9F4F-F695892C8086.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/3BBF9823-01C9-46AD-9107-94E311646F32.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/88761553-0899-4E14-998B-53271DF49FEC.jpg)
Scurvy
![](https://photos.thisispiggy.com/file/wikiFiles/40AFA15E-7689-49B0-9260-CC3AF6B0DEB3.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/6848D004-A946-4518-A4E0-92FFCEC393EA.jpg)
- propeptide added to fibrillar collagens
![](https://photos.thisispiggy.com/file/wikiFiles/8CA6F7FD-36C9-4498-8BAC-062C415CAD8D.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/96C18E5E-A39E-4102-A8C7-228EA7C50ED0.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/FD69544F-199B-4F4C-8224-8896FC0E5932.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/8B90C41F-B182-4755-8302-5B1F7464D331.jpg)
Pathology
![](https://photos.thisispiggy.com/file/wikiFiles/625A9C54-90ED-4655-9894-AB80B906B8A3.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/79EC55FD-74FF-4CD3-8CEC-FE3AF5C92F19.jpg)
Osteogenesis
![](https://photos.thisispiggy.com/file/wikiFiles/B0DBA7D0-7D60-475D-922D-8CD4E88B175C.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/E1A035E7-C46B-4B08-8AF3-32ADD6B08F21.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/3CD25AAD-1255-4B0F-B951-CE062ECD1B5A.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/83F7AEC4-D444-4402-8434-7E95F7A3E784.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/D73AB0EF-F43B-4DE1-BAD5-472E574B4D9B.jpg)
Ehlers Danlos
![](https://photos.thisispiggy.com/file/wikiFiles/AB8982D7-EE75-43D3-937D-C9A5F4F4CB82.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/4C765071-FCB7-464E-B364-F39577148061.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/2124E189-4057-4FA7-B3E3-93B50383F726.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/033D5167-B7E3-463A-A437-5B3647B66DCD.jpg)
Menke
![](https://photos.thisispiggy.com/file/wikiFiles/2C23879E-FCE7-44DE-A486-252FB7963BB1.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/65759BBF-9875-476B-8D14-0A9B4B4EBDFD.jpg)
Elastin
![](https://photos.thisispiggy.com/file/wikiFiles/A5CB7E92-2FD4-40E6-9A07-04D09D88C058.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/DE419102-8713-4C49-A503-015060766101.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/A8EC7D7D-50E8-40AD-B71E-FF9BF31BFAE9.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/EA7A44E5-9C82-475F-BB7F-89286CDD8CCE.jpg)
AAT
![](https://photos.thisispiggy.com/file/wikiFiles/ED592FB8-B677-4AB8-8888-FB544CAD6386.jpg)
Williams
![](https://photos.thisispiggy.com/file/wikiFiles/0D265F72-965E-475A-9B72-677F7CEE158C.jpg)
- elastin important component of aorta
Fibrillin
![](https://photos.thisispiggy.com/file/wikiFiles/3A0C8F7A-92D4-47C4-A568-066624E7DAE2.jpg)
Marfan
![](https://photos.thisispiggy.com/file/wikiFiles/1693D50F-1F9C-46BE-A554-ACEBA0C47300.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/0D5A2385-B3C0-4F48-9A64-590788D9D3BB.jpg)
- CT abnormal, allow pts to grow very tall with long arms
![](https://photos.thisispiggy.com/file/wikiFiles/40024DB2-38B3-447C-BBC1-A68D5E60F58A.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/703680A4-D8D1-40EB-8C28-69FAB2D01B84.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/8F5F1247-168F-47AF-8A43-B26F5EE4AA84.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/F438E0A9-9F86-41C9-894F-630325CDE314.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/9942144E-36EA-4410-B7C4-6BEEA05CB886.jpg)
- weak aortas because weak elastin from fibrillin deficiency
![](https://photos.thisispiggy.com/file/wikiFiles/084F42E2-6190-4078-BE28-E2C11A0A51FA.jpg)
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