19 Biliary Disorders
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Biliary Atresia
![](https://photos.thisispiggy.com/file/wikiFiles/CDDCBA4C-2D35-4B0C-87C7-E219898F8A28.jpg)
Primary Biliary Cirrhosis
![](https://photos.thisispiggy.com/file/wikiFiles/3CAC4B99-B233-4B67-A9D5-0BD33D3567CE.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/353C7E64-74DC-4F1B-8884-88D41638900F.jpg)
- without obstruction/mass/stones
- obstruction inside liver
![](https://photos.thisispiggy.com/file/wikiFiles/653F1952-62C8-4CA1-83D5-332F0F811D8D.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/17CED5ED-B2A9-4A03-8BAF-B692EDCBB1DE.jpg)
- itching and very high alk phos
![](https://photos.thisispiggy.com/file/wikiFiles/41286B12-96D9-44AE-99CC-B41A46A89B34.jpg)
- can't get lipids out in bile
- RUQ US: nl bile duct
![](https://photos.thisispiggy.com/file/wikiFiles/7DBCDC50-E290-4802-82B5-FD6D8EDC4676.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/FFFD023A-D175-4880-B38A-7322F15E5A09.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/DA6B69AE-88C9-49CD-8D5F-E17CFDE6AF43.jpg)
Primary Sclerosing Cholangitis
![](https://photos.thisispiggy.com/file/wikiFiles/6D15155F-EB4A-4773-A23E-0AAD598EA2BD.jpg)
- biliary tree stuck together. Bile can't flow
- primary biliary cirrhosis only intra ducts
- complication of ulcerative colitis
![](https://photos.thisispiggy.com/file/wikiFiles/E4B1F1F9-9019-4D47-9A90-9C21192D670A.jpg)
- scar, fibers form as result of inflammation, then strictures form
Diagnosis
![](https://photos.thisispiggy.com/file/wikiFiles/0E824D07-E95E-447A-A4BC-70527AD33B63.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/9978F00B-14D4-4941-929A-FCC194F24321.jpg)
- fibrous tissues laid down in circles around ducts
![](https://photos.thisispiggy.com/file/wikiFiles/5F272F5B-0BD0-4FE3-BA07-B05A9ABFA620.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/DE6C3B0A-8CE0-4939-81C8-3CEE2E5AE254.jpg)
Treatment
![](https://photos.thisispiggy.com/file/wikiFiles/2ED82258-324E-4425-9618-171A1F20E1CC.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/1DC18EE4-9C68-4E09-A465-77C6377868FD.jpg)
Cholangiocarcinoma
![](https://photos.thisispiggy.com/file/wikiFiles/CD3C9A58-12FF-49BB-B5E4-92775A0BC5FF.jpg)
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