Ammonia
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![](https://photos.thisispiggy.com/file/wikiFiles/0318B2A5-8EAC-4156-A467-E27F67D2CA6C.jpg)
- excess are broken down
- generic way aa metabolized
![](https://photos.thisispiggy.com/file/wikiFiles/77346A93-A596-40B9-9F18-BCA332459C3D.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/B17B4735-99E8-4C54-920A-D7FCEF40405C.jpg)
- amino group passed to a keto to become glutamate
![](https://photos.thisispiggy.com/file/wikiFiles/2D7085D0-D748-410F-A293-628AEEAC8733.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/CD723294-CBD7-4DD7-B851-B87EC2737D6F.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/98444F60-3204-4AEB-AB09-CDB460DF547D.jpg)
Glutamine
![](https://photos.thisispiggy.com/file/wikiFiles/D931424A-D049-4A70-AB3E-BB4D077A314A.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/679F7088-E313-4E10-B9F7-8144FA936E65.jpg)
Alanine
![](https://photos.thisispiggy.com/file/wikiFiles/6E02E3F5-98AB-47D5-99E1-7BA1A5710448.jpg)
- amino group passed to pyruvate to create alanine
![](https://photos.thisispiggy.com/file/wikiFiles/715B8A95-1B56-4319-B2A3-8E4B2A597E06.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/3CA63F06-7659-49A5-9AB5-9A52E7A01513.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/BB55AF7E-0A12-40BF-9D9E-4D0359692396.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/ECE875F4-AA23-4592-9E53-C2E716F5962A.jpg)
- alanine taken to liver but can't be metabolized
Urea
![](https://photos.thisispiggy.com/file/wikiFiles/FFDA5FB2-8857-4734-9A0B-734037EE0ACA.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/BCFD5198-6509-4C85-B06D-33A5B5B02D18.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/8D39A3AC-1030-4C4C-AC4D-46499FF94F7A.jpg)
- high levels of glutamate and acetyl coa in fed state
- activate urea cycle
![](https://photos.thisispiggy.com/file/wikiFiles/4A6655CF-B9DE-47D6-AFB1-E5A62D57D88A.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/5D930236-EC66-4F4D-AB3D-817114F5F6F3.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/122643B9-B474-4520-8799-168247B9E7DA.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/EF24F960-CA76-41DD-BB46-3817720BE9ED.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/0BC1E255-7DD6-44F9-B84E-FA94EBACEC81.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/3AE606AB-BCCB-4CA4-BA9C-11825FDBF403.jpg)
- urea cycle happen in liver
![](https://photos.thisispiggy.com/file/wikiFiles/28B645BD-1AF3-4715-9573-7CAF92593C6C.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/05B1A300-FCAB-48E8-B6C6-91F731F36DF4.jpg)
- if no aa ingested, little aa breakdown
![](https://photos.thisispiggy.com/file/wikiFiles/385EDE92-8EF0-4D2A-938D-E0F2EBC8922B.jpg)
- only used in children
- arginine becomes essential
OTC Deficiency
![](https://photos.thisispiggy.com/file/wikiFiles/7C7E2F00-6346-43FB-B628-A66AFDB5442A.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/9FA2F79E-F0D3-46FD-9EAD-778B896B1169.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/6946D158-777C-47CC-81F7-CA18E68060C1.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/C4182CB0-BA4F-4BCD-BACE-BB32817462BF.jpg)
Citrullinemia
![](https://photos.thisispiggy.com/file/wikiFiles/463306DA-31A2-4356-964F-17E945A3FB11.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/096E0816-E624-430F-98C7-FA444EC83807.jpg)
![](https://photos.thisispiggy.com/file/wikiFiles/8A1758A5-22EE-41F8-A883-46C08FF1406A.jpg)
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